| CASE REPORT |
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| Year : 2009 | Volume
: 3
| Issue : 1 | Page : 13-16 |
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Isolated left ventricular noncompaction: A rare indication of heart transplantation in a young girl
AM Betigeri1, Madhu N Shankar2, KM Cherian2
1 Department of Cardiovascular Pathology, Frontier LifeLine, International Center for Cardio Thoracic and Vascular Diseases, Chennai, India
2 Department of Cardiovascular surgery, Frontier LifeLine, International Center for Cardio Thoracic and Vascular Diseases, Chennai, India
Correspondence Address:
A M Betigeri
International Center for Cardio Thoracic and Vascular Diseases, R-30-C Ambatture Industrial Estate Road, Mogappair Chennai-600101
India
 Source of Support: None, Conflict of Interest: None
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The isolated noncompaction of the left ventricle (IVNC) or “spongy myocardium” is a rare disease. IVNC is characterized by an excessively prominent trabecular meshwork of myocardium and deep intertrabecular recesses due to the arrest in the compaction process of the myocardial fibers in the absence of other structural heart diseases. IVNC can occur in sporadic and in familial patterns. The clinical symptoms depend on the extent of noncompacted cardiac segment. IVNC can lead to decompensated heart failure and may be successfully treated with heart transplantation. The morphological criteria for the diagnosis of this entity remain the subject of debate and are usually based on the findings of the imaging studies. Due to rarity of the disease, we are reporting a pathological finding in a recipient heart. This 9-year-old girl had undergone transcoronary stem cell implantation previously, before undergoing successful orthotropic heart transplantation.
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